Mesenteric lipoblastoma in a girl: report of a case and review of the literature
DOI:
https://doi.org/10.61651/rped.2007v60n3p182-187Abstract
Abdominal masses in children are concerning. Those are challenges for the pediatrician and require accurate and fast diagnosis. Among the bening abdominal masses in the pediatric group are lipoblastomas. Those tumors of mesenchimal origin consist of immature adipocytes mainly located in the extremities; however other locations such as intraabdominal locations are also found. The present case is the report of a mensenteric lipoblastoma in a 19 months old female originally from Piura. The patient was referred to us for work up of giant intraabdominal tumor. Ancillary tests were inconclusive. The diagnosis was made by exploratory laparotomy. The tumor’s weight was 1780 g and pathology revealed its nature.
Superficial or subcutaneous embryonal white fat tumors are classified as lipoblastomas. Lipoblastomatosis are deep or intracavitary embryonal white fat tumors. Cytogenetics reveals chromosal 8 (8q 11 13) abnormalities. The differential diagnosis include other tumors according to the location, such as liposarcoma, rabdosarcoma etc. The differential diagnosis of intraabdominal lipoblastoma also includes nephroblastoma, neuroblastoma, teratoma, etc. Complete surgical excision with 5 years follow up is the preferred therapy. Recurrence is reported in 9 to 33% of cases.
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